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Уровень 1
Уровень 2
Уровень 3
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            [DETAIL_TEXT] => 

Уровень 3: Симптоматика заболеваний

Представляет

Раводин Роман Анатольевич
Дерматовенеролог, дерматоонколог, дерматокосметолог
Доктор медицинских наук, доцент
Категория: первая
Консультирует взрослых и детей
Город: Санкт-Петербург
Стаж: 15 лет
Базовое образование:
Военно-медицинская академия им. С.М. Кирова с золотой медалью, 1999
Дополнительное образование:
Адъюнктура при кафедре кожных и венерических болезней Военно-медицинской академии (2002-2005)
Основное место работы:
ООО "НПЦ ЛОГОДЕРМ", Северо-Западный государственный медицинский университет им. И.И. Мечникова,кафедра дерматовенерологии
Должность:
Доцент
Профессиональный опыт:
Занимается лечением и диагностикой всего спектра дерматовенерологических заболеваний, уделяя особое внимание редким и атипичным формам. При необходимости самостоятельно берёт соскобы и мазки, микроскопирует их и выдаёт заключение. Выполняет лазерное удаление невусов (родинок) и опухолей кожи. Является автором и соавтором более 70 научных работ по дерматовенерологии, включая два изобретения.

Третий уровень содержит 80 двухчасовых занятий и посвящён симптоматике наиболее распространённых дерматовенерологических заболеваний, включая рекомендации по их обследованию и лечению.

Каждое заболевание можно разложить на составляющие его симптомы с учётом их специфичности.

Высокоспецифичные симптомы включают те симптомы, которые наиболее характерны для данного заболевания (являются патогномоничными) и/или встречаются практически всегда при этом заболевании.

Среднеспецифичные – те симптомы, которые могут встречаться при данном заболевании, но в ряде случаев могут отсутствовать.

Низкоспецифичные − симптомы, которые нехарактерны для данной нозологии.

Каждый симптом, который может быть визуализирован, снабжён фотографиями.

Общее описание заболевания включает также его клинические фотографии, а рекомендации по обследованию снабжены изображениями гистологических и микроскопических препаратов.

Рекомендации по лечению основаны на национальных клинических рекомендациях.

После изучения заболевания доступен промежуточный тест для  самопроверки.

По окончании ознакомления с материалами уровня Вам предлагается пройти итоговый тест.

[~DETAIL_TEXT] =>

Уровень 3: Симптоматика заболеваний

Представляет

Раводин Роман Анатольевич
Дерматовенеролог, дерматоонколог, дерматокосметолог
Доктор медицинских наук, доцент
Категория: первая
Консультирует взрослых и детей
Город: Санкт-Петербург
Стаж: 15 лет
Базовое образование:
Военно-медицинская академия им. С.М. Кирова с золотой медалью, 1999
Дополнительное образование:
Адъюнктура при кафедре кожных и венерических болезней Военно-медицинской академии (2002-2005)
Основное место работы:
ООО "НПЦ ЛОГОДЕРМ", Северо-Западный государственный медицинский университет им. И.И. Мечникова,кафедра дерматовенерологии
Должность:
Доцент
Профессиональный опыт:
Занимается лечением и диагностикой всего спектра дерматовенерологических заболеваний, уделяя особое внимание редким и атипичным формам. При необходимости самостоятельно берёт соскобы и мазки, микроскопирует их и выдаёт заключение. Выполняет лазерное удаление невусов (родинок) и опухолей кожи. Является автором и соавтором более 70 научных работ по дерматовенерологии, включая два изобретения.

Третий уровень содержит 80 двухчасовых занятий и посвящён симптоматике наиболее распространённых дерматовенерологических заболеваний, включая рекомендации по их обследованию и лечению.

Каждое заболевание можно разложить на составляющие его симптомы с учётом их специфичности.

Высокоспецифичные симптомы включают те симптомы, которые наиболее характерны для данного заболевания (являются патогномоничными) и/или встречаются практически всегда при этом заболевании.

Среднеспецифичные – те симптомы, которые могут встречаться при данном заболевании, но в ряде случаев могут отсутствовать.

Низкоспецифичные − симптомы, которые нехарактерны для данной нозологии.

Каждый симптом, который может быть визуализирован, снабжён фотографиями.

Общее описание заболевания включает также его клинические фотографии, а рекомендации по обследованию снабжены изображениями гистологических и микроскопических препаратов.

Рекомендации по лечению основаны на национальных клинических рекомендациях.

После изучения заболевания доступен промежуточный тест для  самопроверки.

По окончании ознакомления с материалами уровня Вам предлагается пройти итоговый тест.

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Уровень 4
Уровень 5
Уровень 6
Уровень 7
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Уровень 13

Акродерматит хронический (Аллопо)

Определение

Акродерматит хронический (Аллопо) – это хронический воспалительный дерматоз, в настоящее время относящийся к одной из форм локализованного пустулёзного псориаза, который проявляется рецидивирующими высыпаниями стерильных пустул на кончиках пальцев кистей и/или стоп.

Синонимы

acrodermatitis continua suppurativa Hallopeau, акродерматит стойкий пустулёзный Аллопо, акропустулёз, пустулёзный акродерматит, персистирующий акродерматит.

Эпидемиология

Возраст: заболевание чаще всего начинается в возрасте 17-50 лет, хотя может встречаться и у детей.
Пол: женщины болеют чаще мужчин.

Анамнез

Акродерматит хронический (Аллопо) начинается с воспаления кожи ногтевых валиков дистальной фаланги большого пальца кисти (реже других пальцев кисти или большого пальца стопы), впоследствии распространяясь на другие пальцы кистей (стоп). Ногтевые валики отёчны, гиперемированы и болезненны, из-под них нередко выделяется гной – клиническая картина напоминает гнойную паронихию. Позднее на поверхности воспаленной кожи дистальных фаланг появляются пустулы величиной с булавочную головку, слегка увеличивающиеся в размерах и частично сливающиеся друг с другом с образованием гнойных озер. Заболевание протекает волнообразно: на фоне уже существующих или разрешившихся высыпаний появляются свежие гнойнички, которые впоследствии подсыхают с образованием корочек и чешуек. При насильственном отторжении корок образуются болезненные эрозии. После разрешения высыпаний остаётся атрофичная блестящая красноватая кожа. Образование пустул на ногтевом ложе часто приводит к ониходистрофиям или полной отслойке ногтевых пластинок с последующим прекращением их роста (анонихии). При тяжелом и длительном течении вследствие остеолиза могут укорачиваться дистальные фаланги пальцев. Патологический процесс может оставаться локализованным, но иногда имеет тенденцию распространяться проксимально, захватывая весь палец, кисть (стопу), предплечье. В ряде случаев акродерматит хронический (Аллопо) может сочетаться с генерализованным пустулёзным псориазом Цумбуша.

Течение

острое начало с последующим хроническим рецидивирующим многолетним течением. Ремиссии, как правило, носят нестойкий характер ввиду рефрактерности (устойчивости) к проводимому лечению. В случае сочетания с генерализованным пустулёзным псориазом Цумбуша заболевание может закончиться летально.

Этиология

не установлена.

Предрасполагающие факторы

1) травматизация (повреждение) кожи ногтевых валиков;
2) инфекция (паронихия) ногтевых валиков;

Жалобы

На наличие болезненных высыпаний гнойничков на коже ногтевых фаланг пальцев кистей и/или стоп, реже на зуд и жжение в месте высыпаний, иногда на боли и скованность в суставах кистей (стоп). Часто больных беспокоит изменение или выпадение ногтей.

Дерматологический статус

процесс поражения кожи носит распространённый и, как правило, симметричный характер, элементы сыпи склонны к слиянию.

Элементы сыпи на коже

  • равномерно окрашенные воспалительные пятна красного цвета около 2 см в диаметре (иногда и больших размеров), округлой, полосовидной или неправильной формы, с резкими или размытыми очертаниями, поверхность которых может пластинчато шелушиться. При поскабливании пятен нередко определяется симптом скрытого мокнутия – появление отдельных микроэрозий, отделяющих серозный экссудат. При диаскопии (надавливании прозрачным стеклом) пятна полностью исчезают. В дальнейшем на их поверхности образуются пустулы, иногда пузырьки, трансформирующиеся в пустулы. Пятна сущесвуют длительно, могут увеличиваться по периферии, а при своём разрешении нередко оставляют атрофические изменения. 
  • полушаровидные гнойнички (пустулы) от 0,2 до 0,5 см в диаметре, располагающиеся на фоне гиперемированной кожи, склонные к слиянию, которые подсыхают с образованием корок и в последующем бесследно разрешаются;
  • иногда на фоне воспалительно изменённой кожи встречаются пузырьки с гладкой поверхностью и серозным содержимым, от 0,2 до 0,5 см в диаметре, превращающиеся в гнойнички или вскрывающиеся с образованием эрозий;
  • корки желтовато-серого или бурого цвета, располагающиеся на месте подсохших пустул на фоне воспалённой кожи, которые могут отторгаться с образованием эрозий;
  • болезненные эрозии, возникающие на месте корок (при их насильственном отторжении), от 0,2 до 0,5 см в диаметре, располагающиеся на фоне воспалённой кожи, которые в дальнейшем разрешаются бесследно;
  • на фоне сухой, воспалённой, атрофичной  кожи и корок могут формироваться болезненные трещины, которые впоследствии эпителизируются и уходят бееследно;
  • пластинчатые чешуйки серебристо-белого, серого или цвета нормальной кожи на поверхности воспалительных пятен или в местах ранее бывших высыпаний при их разрешении;
  • очаговая или диффузная (захватывает две и более анатомические области, если речь идёт о нескольких пальцах) вторичная атрофия кожи, развивающаяся на месте высыпаний при длительном течении воспалительного процесса, по  глубине − глубокая (может сопровождаться укорочением дистальных фаланг пальцев, прекращением роста ногтей), по цвету − красного или желтовато-бурого (восковидного) цвета;

Элементы сыпи на слизистых

Отсутствуют.

Локализация

дистальные фаланги больших пальцев кистей (реже других пальцев кистей или больших пальцев стоп), весь палец (пальцы), кисти (стопы), предплечья, редко высыпания носят диссеминированный характер – в этом случае заболевание сочетается с генерализованным пустулёзным псориазом Цумбуша.

Дифференциальный диагноз

С пустулёзным псориазом ладоней и подошв; дисгидротической формой микоза стоп, осложнённой вторичной инфекцией; ладонно-подошвенным пустулёзом; пустулёзной токсикодермией; вирусной пузырчаткой полости рта и конечностей; экземой кистей и стоп, осложнённой вторичной инфекцией.

Сопутствующие заболевания

артрит, остеолиз дистальных фаланг пальцев, невротические расстройства, генерализованный пустулёзный псориаз Цумбуша.

Диагноз

Наличие пустулёзных высыпаний на дистальных фалангах пальцев кистей и/или стоп в сочетании с отрицательными результатами посева содержимого пустул. В сомнительных случаях для подтверждения диагноза проводят гистологическое исследование биоптата пораженной кожи.

Патогенез

Не изучен. 

Дополнительные исследования:

Гистологическое исследование:
в роговом слое эпидермиса наблюдается паракератоз, очаговый ортокератоз, микроабсцессы Мунро (скопление нейтрофильных лейкоцитов), зернистый слой полностью отсутствует. В нижней части мальпигиевого слоя – спонгиоформные пустулы Когоя, спонгиоз, гиперплазия и удлинение эпидермальных отростков, а также супрапапиллярное истончение эпидермиса. Отростки эпидермиса внизу колбообразно утолщены с наличием лимфоцитарной инфильтрации в верхней части дермы. Капилляры сосочков и сосуды поверхностного сплетения расширены и окружены смешанным инфильтратом из нейтрофилов и лимфоцитов, имеются также экстравазаты эритроцитов. Отмечается также эпидермотропизм лейкоцитов, особенно в супрапапиллярных зонах. Бактериальный посев содержимого пустул не дает роста микроорганизмов, т.к. они стерильны.

Вирусологическое исследование в культуре клеток – отрицательно и позволяет провести дифференциальный диагноз с вирусной пузырчаткой полости рта и конечностей.

Микроскопическое исследование соскоба кожи из очага поражения – отрицательно и позволяет провести дифференциальный диагноз с дисгидротической формой микоза стоп.

Рентгенография кистей и стоп:
атрофия и остеолиз дистальных фаланг, артропатия межфаланговых суставов.


Диагноз

Наличие пустулёзных высыпаний на дистальных фалангах пальцев кистей и/или стоп в сочетании с отрицательными результатами посева содержимого пустул. В сомнительных случаях для подтверждения диагноза проводят гистологическое исследование биоптата пораженной кожи.

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